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Catena respiratoria umana


respiratory chain picture          
Componenti della fosforilazione ossidativa codificate dal DNA mitocondriale codificate dal DNA nucleare
Complesso I.

 NADH-deidrogenasi

MTND1, MTND2, MTND3, MTND4, MTND4L, MTND5, MTND69.6k_sub, AQDQ, NDUFA10, NDUFA1, NDUFA2, NDUFA3, NDUFA4, NDUFA5, NDUFA6, NDUFA7, NDUFA8, NDUFA9, NDUFAB1, NDUFB10, NDUFB1, NDUFB2, NDUFB3, NDUFB4, NDUFB5, NDUFB6, NDUFB7, NDUFB8, NDUFB9, NDUFC1, NDUFC2, NDUFS1, NDUFS2, NDUFS3, NDUFS5, NDUFS6, NDUFS7, NDUFS8, NDUFV1, NDUFV2, NDUFV3
Complesso II. Succinato deidrogenasi SDH1, SDH2, SDHC, SDHD
Complesso III. Citocromo b-c1 MTCYBCOX4, CYB5 erythrocite, CYB5 microsomal, CYC1, UQCRB, UQCRC1, UQCRC2, UQCRFS1, UQCRH
Complesso IV. Citocromo c ossidasi MTCO1, MTCO2, MTCO3COX5A, COX5B, COX6A1, COX6A2, COX6B, COX6C, COX7A1, COX7A2, COX7B cardiac, COX7B ubiquitary, COX7C, COX8
Complesso V.

ATP sintetasi

ATP8, MTATP6ATP5A1, ATP5A2, ATP5AL1, ATP5AL2, ATP5B, ATP5BL1, ATP5BL2, ATP5C1, ATP5C2, ATP5CL1, ATP5CL2, ATP5D, ATP5E, ATP5F1, ATP5G1, ATP5G2, ATP5G3, ATP5I, ATP5J

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